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Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA)

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BGL; CDC4L; LBA; LPS-Responsive Vesicle Trafficking,Beach And Anchor Containing; Beige-like protein; CDC4-like protein

Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA)
CCC L672
HGNC 1742
MGI 1933162
PubMed 22721650
RGD 1311428
UniProt P50851
Wiki LRBA
Patients with Chediak-Higashi syndrome (CHS1) suffer from a systemic immunodeficiency involving defects in polarized trafficking of vesicles in a number of immune system cell types. In mouse, this syndrome is reproduced in strains with a mutation in the 'beige' gene that results in proteins lacking the BEACH (beige and CHS1) domain and C-terminal WD repeats. LRBA contains key features of both beige/CHS1 and A kinase anchor proteins .
The alpha isoform has 5 WD repeats, while the beta isoform has 3 and the gamma isoform lacks WD repeats. The 2,863-amino acid human LRBA protein is 85% identical to the mouse protein, and they have homology to a Drosophila anchor protein, Akap550.

Organism species: Homo sapiens (Human)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) CLIA Kit Customized Service Offer
n/a ELISA Kit for Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) ELISA Kit Customized Service Offer

Organism species: Mus musculus (Mouse)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) CLIA Kit Customized Service Offer
n/a ELISA Kit for Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) ELISA Kit Customized Service Offer

Organism species: Rattus norvegicus (Rat)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) CLIA Kit Customized Service Offer
n/a ELISA Kit for Lipopolysaccharide Responsive And Beige Like Anchor Protein (LRBA) ELISA Kit Customized Service Offer
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  16. "The consensus coding sequences of human breast and colorectal cancers." Science 314:268-274(2006) [PubMed] [Europe PMC] [Abstract]
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