![Sucrase Isomaltase (SI)](/upload/item/img/Sucrase-Isomaltase-(SI)-93186.jpg)
Congenital sucrase-isomaltase deficiency is an example of a disease in which mutation results in transport-incompetent molecules. sucrase-isomaltase is not transported to the brush border membrane but accumulates as a mannose-rich precursor in the endoplasmic reticulum, ER-Golgi intermediate compartment, and the cis-Golgi, where it is finally degraded.
The enzyme consists of 2 subunits which are synthesized as a single chain mannose-rich precursor. From studies of the cDNA, the human protein has 83% identity with the rabbit enzyme. In addition to the previously reported homology with lysosomal alpha-glucosidase, the sucrase and isomaltase subunits appear to be homologous to a yeast glucoamylase.
Organism species: Homo sapiens (Human)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | RPD186Hu01 | Recombinant Sucrase Isomaltase (SI) | Positive Control; Immunogen; SDS-PAGE; WB. |
Antibodies | PAD186Hu01 | Polyclonal Antibody to Sucrase Isomaltase (SI) | WB; IHC; ICC; IP. |
LAD186Hu71 | Biotin-Linked Polyclonal Antibody to Sucrase Isomaltase (SI) | WB; IHC; ICC. | |
LAD186Hu81 | FITC-Linked Polyclonal Antibody to Sucrase Isomaltase (SI) | WB; IHC; ICC; IF. | |
MAD186Hu21 | Monoclonal Antibody to Sucrase Isomaltase (SI) | WB; IHC; ICC; IP. | |
MAD186Hu24 | Monoclonal Antibody to Sucrase Isomaltase (SI) | WB; IHC; ICC; IP. | |
MAD186Hu22 | Monoclonal Antibody to Sucrase Isomaltase (SI) | WB; IHC; ICC; IP. | |
MAD186Hu23 | Monoclonal Antibody to Sucrase Isomaltase (SI) | WB; IHC; ICC; IP. | |
Assay Kits | SED186Hu | ELISA Kit for Sucrase Isomaltase (SI) | Enzyme-linked immunosorbent assay for Antigen Detection. |
Organism species: Mus musculus (Mouse)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | n/a | Recombinant Sucrase Isomaltase (SI) | Recombinant Protein Customized Service Offer |
Antibodies | n/a | Monoclonal Antibody to Sucrase Isomaltase (SI) | Monoclonal Antibody Customized Service Offer |
n/a | Polyclonal Antibody to Sucrase Isomaltase (SI) | Polyclonal Antibody Customized Service Offer | |
Assay Kits | n/a | CLIA Kit for Sucrase Isomaltase (SI) | CLIA Kit Customized Service Offer |
n/a | ELISA Kit for Sucrase Isomaltase (SI) | ELISA Kit Customized Service Offer |
Organism species: Rattus norvegicus (Rat)
CATALOG NO. | PRODUCT NAME | APPLICATIONS | |
Proteins | n/a | Recombinant Sucrase Isomaltase (SI) | Recombinant Protein Customized Service Offer |
Antibodies | n/a | Monoclonal Antibody to Sucrase Isomaltase (SI) | Monoclonal Antibody Customized Service Offer |
n/a | Polyclonal Antibody to Sucrase Isomaltase (SI) | Polyclonal Antibody Customized Service Offer | |
Assay Kits | n/a | CLIA Kit for Sucrase Isomaltase (SI) | CLIA Kit Customized Service Offer |
n/a | ELISA Kit for Sucrase Isomaltase (SI) | ELISA Kit Customized Service Offer |
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