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Fucosidase Alpha L1, Tissue (FUCa1)

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A-FU; aFU; Alpha-L-Fucosidase; Alpha-L-fucoside fucohydrolase 1

Fucosidase Alpha L1, Tissue (FUCa1)
CCC A807
HGNC 4006
MGI 95593
PubMed 8076935
RGD 2636
UniProt P04066
Wiki Fucosidase

This enzyme is also called alpha-fucosidase. This enzyme participates in n-glycan degradation and glycan structures - degradation.

Alpha-Fucosidase is an enzyme that breaks down fucose.Fucosidosis is an autosomal recessive lysosomal storage disease caused by defective alpha-L-fucosidase with accumulation of fucose in the tissues. Different phenotypes include clinical features such as neurologic deterioration, growth retardation, visceromegaly, and seizures in a severe early form; coarse facial features, angiokeratoma corporis diffusum, spasticity and delayed psychomotor development in a longer surviving form; and an unusual spondylometaphyseoepiphyseal dysplasia in yet another form.

Organism species: Homo sapiens (Human)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPA807Hu01 Recombinant Fucosidase Alpha L1, Tissue (FUCa1) Positive Control; Immunogen; SDS-PAGE; WB.
APA807Hu01 Active Fucosidase Alpha L1, Tissue (FUCa1) Cell culture; Activity Assays.
Antibodies PAA807Hu01 Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) WB; IHC; ICC; IP.
MAA807Hu22 Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) WB; IHC; ICC; IP.
Assay Kits SEA807Hu ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) Enzyme-linked immunosorbent assay for Antigen Detection.

Organism species: Mus musculus (Mouse)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPA807Mu01 Recombinant Fucosidase Alpha L1, Tissue (FUCa1) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies PAA807Mu01 Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) WB; IHC; ICC; IP.
Assay Kits n/a CLIA Kit for Fucosidase Alpha L1, Tissue (FUCa1) CLIA Kit Customized Service Offer
n/a ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) ELISA Kit Customized Service Offer

Organism species: Rattus norvegicus (Rat)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPA807Ra01 Recombinant Fucosidase Alpha L1, Tissue (FUCa1) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies PAA807Ra01 Polyclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) WB; IHC; ICC; IP.
MAA807Ra21 Monoclonal Antibody to Fucosidase Alpha L1, Tissue (FUCa1) WB; IHC; ICC; IP.
Assay Kits SEA807Ra ELISA Kit for Fucosidase Alpha L1, Tissue (FUCa1) Enzyme-linked immunosorbent assay for Antigen Detection.
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